ISSN: 1300-7734
Dil: Türkçe, İngilizce
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Rendu-osler-weber Syndrome: Case Report
Dr. Serhat ATILGAN,a Dr. Gülten ÜNLÜ,a Dr. Ferhan YAMAN,a Dt. Eylül ERGÜVENa
aAğız-Diş-Çene Hastalıkları ve Cerrahisi ABD, Dicle Üniversitesi Dişhekimliği Fakültesi, DİYARBAKIR
Hereditary hemorrhagic telangiectasia (HHT), also known as Rendu-Osler-Weber disease, is an autosomal dominant disorder characterized by epistaxis, coetaneous telangiectasia, and visceral arteriovenous malformations. The characteristic lesions in this disorder are telangiectases that consist of focal dilatations of post capillary venules and arteriovenous malformations. Recurrent epistaxis often restricts daily life. AVMs can cause serious complications if located in the lungs, liver, or brain. Gastrointestinal and urinary bleeding can be occur. Depending on these bleeding can be develop anemia. Superficial vascular structure with thin wall will show in histopathology.
In this study Rendu-Osler-Weber Syndrome thought to presented and discussed because of rarely appearing.Keywords: Telangiectasia, hereditary hemorrhagic;mouth diseasesTurkiye Klinikleri J Dental Sci 2007, 13:135-138
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